1. Anti-Fibrotic Action
Pirfenidone reduces pathological scar formation by inhibiting key profibrotic pathways:
- Downregulates TGF-β (Transforming Growth Factor-β): TGF-β is a central cytokine in skin fibrosis and scarring. Pirfenidone inhibits its production, blocking excessive fibroblast proliferation and myofibroblast differentiation.
- Suppresses Collagen Production: Pirfenidone significantly reduces collagen I and III expression, curbing extracellular matrix (ECM) accumulation.
- Modulates other Growth Factors: It lowers the levels of:
- '
- Platelet-Derived Growth Factor (PDGF)
- Vascular endothelial growth factor (VEGF)
- Fibroblast Growth Factor β (FGF-β)
2. Anti-Inflammatory Action
Inflammation is a precursor to fibrosis. Pirfenidone helps modulate this early response:
- Inhibits Proinflammatory Chemokines and Cytokines, most notably tumour necrosis factor (TNF)-α, interleukin (IL)-4, IL-13, IL-1β, IL-6, IL-8, and IL-12
- Promotes Anti-inflammatory Cytokines: Enhances IL-10 activity, which limits prolonged inflammatory cycles.
3. Antioxidant Action
Oxidative stress contributes to chronic inflammation and fibrosis.
- Pirfenidone scavenges free radicals and decreases Reactive Oxygen Species (ROS) levels in tissue microenvironment.
Impact of Pirfenidone
|
Cellular Function |
Effect of Pirfenidone |
|
Fibroblast Proliferation |
Reduced |
|
Myofibroblast Differentiation |
Inhibited |
|
Collagen Synthesis |
Reduced |
|
Cytokine Expression |
Reduced |
|
Oxidative Stress |
Reduced |
Summary
Pirfenidone acts at multiple levels to prevent and reverse scar formation:
- Interrupts fibrotic signaling (TGF-β, PDGF)
- Modulates immune response
- Reduces collagen deposition
- Improves wound remodeling
References
- Knighton K, Babun A, Turney J, Evans B, Sehgal I. Pirfenidone in Skin Fibrosis and Scarring: From Bench Insights to Clinical Data. Med Sci (Basel). 2025 Aug 20;13(3):148
- Aimo A, Cerbai E, Bartolucci G, Adamo L, Barison A, Lo Surdo G, Biagini S, Passino C, Emdin M. Pirfenidone is a cardioprotective drug: Mechanisms of action and preclinical evidence. Pharmacol Res. 2020 May;155:104694
- Aimo A, Spitaleri G, Nieri D, Tavanti LM, Meschi C, Panichella G, Lupón J, Pistelli F, Carrozzi L, Bayes-Genis A, Emdin M. Pirfenidone for Idiopathic Pulmonary Fibrosis and Beyond. Card Fail Rev. 2022 Apr 14;8:e12
- Babariya H, Gaidhane SA, Acharya S, Kumar S. Pirfenidone as a Cornerstone in the Management of Fibrotic Interstitial Lung Diseases and Its Emerging Applications: A Comprehensive Review. Cureus. 2024 Sep 30;16(9):e70497
- Visner GA, Liu F, Bizargity P, Liu H, Liu K, Yang J, Wang L, Hancock WW. Pirfenidone inhibits T-cell activation, proliferation, cytokine and chemokine production, and host alloresponses. Transplantation. 2009 Aug 15;88(3):330-8
- Dai Z, Jiang Y, Guo H, Lu Y, Chen W, Liang T. Pirfenidone Ameliorates Hypertrophic Scar Through Inhibiting Proliferation and Migration of Fibroblasts by Regulating the Wnt/GSK-3β/β-Catenin Signaling Pathway. J Burn Care Res. 2025 Aug 30;46(4):854-861
- Torre A, Martínez-Sánchez FD, Narvaez-Chávez SM, Herrera-Islas MA, Aguilar Salinas CA, Córdova-Gallardo J. Pirfenidone use in fibrotic diseases: What do we know so far? Immun Inflamm Dis. 2024 Jul;12(7):e1335.